Abstract

In this report, we present a rare case of Ewing's sarcoma with a peripheral primitive neuroectodermal tumor (ES/PNET) arising from presacral soft tissue in a 14-year-old boy. He had a previous long history for 2 years ago: dramatically started by progressive, worsening low back pain three months of trauma; to ending with a paraplegia associated with urine and stool incontinence. He was presented to a hospital in the capital Sana'a, Yemen. Computed tomography (CT) scan and magnetic resonance imaging (MRI) showed a soft tissue mass in presacral area with bone erosion and destruction; staging chest radiographs and CT showed no evidence of metastatic disease. While, his histologic testing confirmed presence of " ES " as small, round, blue cells. The patient subjected to chemotherapy for one year followed by radiotherapy and he got improved. He stopped radiotherapy for four months led to rapid progressive deterioration ended by brain metastasis and the patient died through three months.

Keywords: Ewing's sarcoma, Presacral soft tissue, Case report, Yemen

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